Introduction
- Cutaneous melanocytic tumor with CRTC1::TRIM11 fusion (CMTCT) is a rare dermatological neoplasm that has not yet been formally recognized by the World Health Organization.
- At present, our knowledge of this disease is limited to single reports and a series of 41 cases with limited follow-up information.
- It is typically described as a skin lesion expressing melanocytic makers, often leading to its misdiagnosis as melanoma or clear cell sarcoma.
- CMTCT is regarded as an indolent tumor with infrequent recurrence after complete surgical excision.
- However, we present a case with uncommon sinonasal presentation and metastasis after multiple resections.